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GONZÁLEZ-GRANADO , Luis I.

Last name: GONZÁLEZ-GRANADO

First name: Luis I.

September 26, 2022 (v1)

Publication

Metadata-only

Primary Immune Regulatory Disorders With an Autoimmune Lymphoproliferative Syndrome-Like Phenotype: Immunologic Evaluation, Early Diagnosis and Management

López-Nevado, Marta González-Granado, Luis I. Ruiz-García, Raquel

Primary immune regulatory disorders (PIRD) are associated with autoimmunity, autoinflammation and/or dysregulation of lymphocyte homeostasis. Autoimmune lymphoproliferative syndrome (ALPS) is a PIRD due to an apoptotic defect in Fas-FasL pathway and characterized by benign and chronic lymphoproliferation, autoimmunity and increased risk of...

Uploaded on: December 4, 2022