ObjectiveTo assess performance of the 2016 macrophage activation syndrome (MAS) classification criteria for patients with systemic juvenile idiopathic arthritis (JIA) who develop MAS while treated with biologic medications.MethodsA systematic literature review was performed to identify patients with MAS while being treated with interleukin...
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2018 (v1)PublicationUploaded on: April 14, 2023
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2020 (v1)Publication
To study growth and puberty in a multi-national longitudinal prospective cohort of juvenile dermatomyositis (JDM).
Uploaded on: April 14, 2023 -
2024 (v1)Publication
Objective To develop parent- and child-centred versions of the Juvenile Arthritis Disease Activity Score (JADAS) and to provide preliminary evidence of their validity. Methods Validation analyses were conducted on two large multinational datasets of patients with juvenile idiopathic arthritis (JIA) and included assessment of construct validity,...
Uploaded on: October 21, 2024 -
2024 (v1)Publication
Objectives: The aim of the study was to establish an international multicenter registry to collect data on patients with Multisystem Inflammatory Syndrome in Children (MIS-C), in order to highlight a relationship between clinical presentation, age of onset and geographical distribution on the clinical outcome.Study design: Multicenter...
Uploaded on: October 21, 2024 -
2016 (v1)Publication
Objective: To identify which laboratory tests that change over time are most valuable for the timely diagnosis of macrophage activation syndrome (MAS) complicating systemic juvenile idiopathic arthritis (sJIA). Methods: A multistep process, based on a combination of expert consensus and analysis of real patient data, was conducted. A panel of...
Uploaded on: April 14, 2023 -
2017 (v1)Publication
Objective To develop and validate a diagnostic score that assists in discriminating primary hemophagocytic lymphohistiocytosis (pHLH) from macrophage activation syndrome (MAS) related to systemic juvenile idiopathic arthritis. Study design The clinical, laboratory, and histopathologic features of 362 patients with MAS and 258 patients with pHLH...
Uploaded on: April 14, 2023